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. 2011 Feb 23;8:14. doi: 10.4314/pamj.v8i1.71064

Table 2: Number and percentage of inborn errors of metabolism in a population of children born with inborn errors of metabolism from 2006 to 2009 in the neonatology section, Maternity Hospital, Al Ahsa, Eastern Region, Saudi Arabia.

Total confirmed cases of metabolic errors
No of Screened Live births Confirmed Cases Type No %
3-methylcrotonyl-CoA carboxylase (3– MCC) 13 20.63
Biotinidaze deficiency 12 19.05
Medium Chain acyl Coenzyme A Dehydrogenase (MCAD) 5 7.94
Glutaric Aciduria 1 1.59
Glutaric Academia type 2 4 6.35
Probionic Acidemia 1 1.59
Homocysteinuria 2 3.17
Primary Carnitin deficiency 1 1.59
37168 63 (0.17%)
Nonketotic hyperglycinaemia (NKH) 2 3.17
Galactosemia 2 3.17
Phenyl Ketonuria (PKU) 1 1.59
Methylmalonic acidaemia (MMA) 2 3.17
Multiple corboxylase deficiency 1 1.59
Citrulinemia 1 1.59
Hypothyroidism 12 19.05
Congenital adrenal hyperplasia (CAH) 3 4.76