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. Author manuscript; available in PMC: 2012 Oct 20.
Published in final edited form as: Neuron. 2011 Sep 21;72(2):245–256. doi: 10.1016/j.neuron.2011.09.011

Figure 1. Neuropathology in familial FTD/ALS linked to chromosome 9p (family VSM-20).

Figure 1

(A, B) FTLD-TDP characterized by TDP-43 immunoreactive neuronal cytoplasmic inclusions and neurites in (A) neocortex and (B) hippocampal dentate granule cell layer. (C) TDP-34 immunoreactive neuronal cytoplasmic inclusions in spinal cord lower motor neurons, typical of ALS. (D) Numerous neuronal cytoplasmic inclusions and neurites in cerebellar granular layer immunoreactive for ubiquitin but not TDP-43. Scale bar: (A) 15 μm, (B) 30 μm, (C) 100 μm, (D) 12 μm.