Table 2.
Location | No. of cases | Case definition | Rate per 100,000 per year | 95% CI |
---|---|---|---|---|
Rochester, MN (Knopman et al. 2004)a | 4 | bvFTD+PPA | 4.1 (age range, 40–69) | 1.1 to 10.4 |
Cambridgeshire UK (Mercy et al. 2008)b | 16 | bvFTD+PPA | 3.5 (age range, 45–64) | 2.0 to 5.7 |
Girona, Spain (Garre-Olmo et al. 2010)c | 14 | bvFTD+semantic dementia | 2.7 (age range, 45–64) | 1.5 to 4.6 |
All cases between ages 40 and 69 years
1/16 cases < age 45 years. Only ages <65 years were considered
Of 70 cases of bvFTD or semantic dementia, 14 were under age 65 at onset