Table 1. Concentrations of urine organic acids (mmole/mole creatine) at different age.
Patient age: | 2-Methyl-3-hydroxybutyric acid | Tiglylglycine |
8 y 4 m | 31 | 32 |
8 y 8 m | 18 | 9 |
10 y 3 m | 152 | 66 |
10 y 4 m | 80 | 40 |
Normal children (age: 2 to 12-year-old) | <14 | <6 |