Figure 4. Crystal structures of human α-GAL bound to pharmacological chaperones.
(a) and (b) show σA-weighted 2Fo-Fc electron density maps of DGJ- and galactose-soaked crystals of wild-type human α-GAL, and (c) shows the D170A mutant α-GAL with DGJ bound. All maps are contoured at 1.8σ with the ligand density colored red for clarity. (d) shows a superposition of the (a) and (b), highlighting the key interaction between the ligand and the D170 carboxylate. See also Table S3.