Table 1.

Clinical features of patients at presentation

Number	Sex	Age, Years	Duration of Symptoms	Anti-MPO	Anti-PR3	Arthralgia	Skin Lesions	Fever/Night Sweats	Weight Loss	Lethargy	Myalgia	ENT	Leukopenia	Ear Lesions	Pulmonary	Oral Ulceration
1	F	44	3 wk	1050		+	+	+	–	+	+	–	–	+	–	–
2	M	55	n/a	1553	172	–	–	–	+	–	–	–	–	–	–	–
3	M	43	28 wk	10,103		+	–	+	+	–	+	+	–	–	+	–
4	F	46	4 wk	132		+	+	+	+	+	–	–	–	–	+a	–
5	M	46	>12 wk	7655		+	+	–	–	–	–	–	–	+	–	–
6	F	57	28 wk	1127	8601	+	+	–	–	–	+	+	+	+	–	–
7	F	50	6 wk	24,986		+	–	+	–	+	+	+	+	–	–	+
8	F	53	12 wk	19,797	230	+	+	+	+	+	+	–	+	–	–	–
9	F	50	8 wk	1826		+	+	–	–	–	+	–	–	–	–	–
10	M	41	6 wk	12,698		+	+	–	–	+	+	+	–	+	–	+
11	M	42	32 wk	1715	118	+	–	+	+	–	+	+	–	–	+a	–
12	F	49	7 wk	4711		+	–	–	+	+	–	+	–	–	–	+
13	F	36	8 wk	18		+	+	–	–	+	+	–	–	–	+	–
14	F	29	12 wk	1152	153	–	+	+	+	+	–	+	+b	+	–	+
15	F	52	n/a	1741	342	–	+	+	–	–	–	–	+	–	–	–
16	F	51	12 wk	1075	201	+	+	–	–	–	–	+	–	–	–	–
17	M	47	8 wk	12,415	522	+	+	–	–	–	+	–	–	–	–	–
18	M	43	24 wk	2406	49	+	–	–	–	+	–	–	–	–	–	–

n/a, not available; ENT, Ear, Nose, Throat.

^aPulmonary hemorrhage.

^bTreatment of neutropenia with granulocyte macrophage colony-stimulating factor prior to diagnosis.