Table 2.

Clinical aspects of linear scleroderma en coup de sabre (LScs) and Parry-Romberg syndrome (PRS).

	LScs	PRS
Skin	Induration and thickening	Not affected
Initial site	Forehead and scalp	Cheek and nose
Spreading pattern	Usually does not spread below the forehead	Usually affects lower face
	Occasionally affects nose, cheek, chin, and neck	Usually restricted to one side
	Occasionally bilateral
Systemic involvement	Yes	No
Intracranial involvement	Yes	Yes