Table II.
Carnitine Profiles in Individuals with PWS, EMO, and sibling controls
N | Total Carnitine (NL range: 35–90 umol/L) | Free Carnitine (NL range: 25–55 umol/L) | Carnitine Esters (NL range: 4–36 umol/L) | Ester/free Ratio (NL range: 0.1–1.0) | |||||
---|---|---|---|---|---|---|---|---|---|
p-value (3-way) | 0.44 | 0.084 | 0.043* | 0.02* | |||||
Mean | Std Dev | Mean | Std Dev | Mean | Std Dev | Mean | Std Dev | ||
PWS | 40 | 43.4 | 9.8 | 29.7 | 9.3 | 13.7 | 6.7 | 0.52 | 0.45 |
Normal weight Controls | 35 | 42.6 | 8.1 | 32.8 | 6.9 | 9.7 | 5.6 | 0.31 | 0.20 |
EMO | 11 | 46.9 | 12.1 | 35.6 | 7.9 | 11.2 | 6.5 | 0.31 | 0.15 |
Pairwise P-values for carnitine esters: PWS vs. controls: p = 0.013 PWS vs. EMO: p=0.25 Controls vs. EMO: p=0.52
Pairwise P-values for esterified to free carnitine ratio: PWS vs. controls: p = 0.0096 PWS vs. EMO: p=0.081 Controls vs. EMO: p=0.97