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. Author manuscript; available in PMC: 2012 Mar 27.
Published in final edited form as: J Clin Endocrinol Metab. 2001 Aug;86(8):3724–3728. doi: 10.1210/jcem.86.8.7755

TABLE 3.

Leu-AIR Tests in patients with non-HI/HA forms of hyperinsulinism

Patient Plasma ammonium (μmol/liter) Baseline blood glucose (mg/dl) Baseline insulin (μU/ml) Leu-AIR (μU/ml)
KATP hyperinsulinism (mean ± SEM; n = 7) 77 ± 4 8.1 ± 1.9 4.7 ± 1.9a
 Range 0–13
Other forms of hyperinsulinism
 Transient neonatal (TN)
  TN-1, 1 wk 19–41 84 13 13
  TN-2, 4 wk 40 109 3.0 2.5
  TN-3, 6 wk 54 82 4.9 4.8
 Congenital, diazoxide-responsive
  CDR-1, 15 yr 25–37 75 7.8 2.1
  CDR-2, 14 months 27 94 9.2 9.0
  CDR-3, 19 months 22–39 67 2.1 19
  CDR-4, 21 months 21–33 68 2.9 45
  CDR-5, 29 months 8–24 64 6.2 85
a

P < 0.05 vs. HI/HA patients.