Table 2.

FSHD clinical onset: the predominant types.^a

Facio-scapulo-humeral onset
Scapulo-humeral symptoms	80/122
M/F	56/24
Age at onset	24 years (range: 5–60)
Unilateral	32/80
Bilateral	48/80
Signs of facial weakness	78/80
Eco RI fragment (mean)	24 kb (range: 14–38)
Facial symptoms	8/122
M/F	3/5
Age at onset	8 (range: 4–23)
Signs of scapulo-humeral weakness	8/8
Eco RI fragment (mean)	18 kb (range: 14–30)
Foot drop onset	16/122
M/F	9/7
Age at onset	27 (range: 10–53)
Unilateral	12/16
Bilateral	4/16
Signs of scapulo-humeral weakness	14/16
Signs of facial weakness	15/16
Eco RI fragment (mean)	27 kb (range: 19–38)

^aThe onset type represented in the table concerns 104 out of 122 patients