Table 1.
Clinical features of 14 patients.
Polyneuropathy | |
Peripheral neuropathy | 14/14 |
Papilledema | 5/10 |
| |
Organomegaly | |
Hepatomegaly | 8/14 |
Splenomegaly | 11/14 |
Lymphadenopathy | 7/14 |
| |
Endocrinopathy | |
Hypothyroidism | 10/14 |
Amenorrhea | 1/14 |
Impotence | 2/14 |
Hypoadrenocorticism | 1/14 |
Hypoparathyroidism | 1/14 |
| |
M-protein | |
IgA λ | 6/13 |
IgA κ | 1/13 |
IgM λ | 1/13 |
IgG λ | 2/13 |
| |
Skin change | |
Hyperpigmentation | 11/14 |
Pruritus | 2/14 |
| |
Edema | |
Peripheral edema | 7/14 |
| |
Effusions | 10/14 |
Ascites | |
Pleural effusion | 8/14 |
Hydropericardium | 8/14 |