Table 2. Creutzfeldt-Jakob disease patients investigated for a possible causal link of their illness with chronic wasting disease of deer and elk, United States^a.

Case no.	Age at death (y)	Year of death	Codon 129	Western blot	Final diagnosis	Eating of venison from CWD-endemic area
1	25	2001	M/V	Type 1	GSS 102	Yes
2	26	2001	M/M	Type 2	CJD	No
3b	28	2002	nd	nd	GSS 102	No
4	28	1997	M/M	nd	CJD	No
5	28	2000	M/V	Type 1	CJD	No
6	30	1999	V/V	Type 1	CJD	No
7	54	2002	V/V	Type 2	CJD	No
8c	55	1999	M/M	Type 1	CJD	No
9d	61	2000	M/M	Type 1	CJD	Yes
10	63	2002	V/V	Type 1	CJD	No
11e	64	2002	M/M	Type 1	CJD	Yes
12	66	2001	M/M	Type 1	CJD	No

^aCWD, chronic wasting disease; GSS, Gerstmann-Sträussler-Scheinker syndrome; CJD, Creutzfeldt-Jakob disease; nd, not done.
^bImmunohistochemical analysis of postmortem brain tissue was consistent with GSS, and a GSS 102 mutation was confirmed in the family.
^cInvestigated as part of a cluster of three case-patients who participated in "wild game feasts" in a cabin owned by one of the decedents.
^dPatient grew up in an area known to be endemic for CWD and ate venison harvested locally; however, the CJD phenotype fits the most common form of sporadic CJD.
^ePatient may have been successful in harvesting two deer since 1996 from a CWD-endemic area, but both deer tested negative for CWD.