Table 3.
Manifestation | % (affected/total) | Median age at diagnosis, years (range) | N | |
Hyperparathyroidism | 88 (22/25) | 39 (19–86) | 22 | |
Pituitary tumor | 28 (7/25) | 40 (18–86) | Acromegaly | 3 |
Prolactinoma | 1 | |||
GH/PRL | 1 | |||
Nonfunctioning adenomas | 2 | |||
Gastroenteropancreatic tumor | 32 (8/25)*) | 35 (19–60) | Gastrinoma | 5 |
Nonfunctioning | 2 | |||
enterochromaffin | 3 | |||
Foregut carcinoids | 16 (4/25)†) | 52 (23–67) | Bronchial | 3 |
Duodenal | 2 | |||
Adrenal gland | 24 (6/25) | 47 (23–86) | Nonfunctioning | 4 |
Bilateral Hyperplasia | 2 |
Two patients presented with gastrinoma and pancreatic neuroendocrine tumor concomitantly.
One patient had lung and duodenal carcinoids.