Table 1.
Characteristics of 83 Probands According to Cardiomyopathy Phenotype
Characteristic | All | HCM | DCM | RCM | LVNC | ARVC |
---|---|---|---|---|---|---|
Gender (n) | ||||||
Male | 38 | 18 | 10 | 3 | 6 | 1 |
Female | 45 | 24 | 15 | 1 | 5 | 0 |
Total | 83 | 42 | 25 | 4 | 11 | 1 |
Age at presentation (%) | ||||||
<1 y | 41 | 45 | 48 | 0 | 27 | 0 |
1 to <6 y | 11 | 5 | 20 | 25 | 9 | 0 |
6 to <13 y | 19 | 19 | 12 | 75 | 18 | 0 |
13 to <18 y | 25 | 26 | 20 | 0 | 36 | 100 |
18 to 21y | 4 | 5 | 0 | 0 | 9 | 0 |
Family history (%) | 36 | 40 | 12 | 75 | 27 | 100 |
Family history of sudden death (%) | 16 | 17 | 4 | 75 | 18 | 100 |