Table 4.

Clinical Characteristics and Echocardiographic Findings in DCM Patients

	Familial n = 6	Metabolic n = 4	Syndromic n = 5	Idiopathic n = 10
NYHA
Class I	0	0	2	2
Class II	0	0	0	0
Class III	1	0	1	0
Class IV	5	4	2	8
Unknown	0	0	0	0
Echocardiography
LVMWT z-score (Range)	1.1 (−0.1 to 2.7)	1.0 (0.2 to 2.6)	0.8 (−0.2 to 2.2)	1.7 (−0.4 to 3.9)
LVEDD z-score (Range)	5.0 (4.1 to 6.8)	3.9 (−0.7 to 8.0)	2.7 (2.2 to 3.7)	4.1 (2.4 to 7.8)
FS z-score (Range)	−9.5 (−13 to −5)	−8.7 (−11 to −5)	−5.3 (−7.8 to −1.5)	−8.4 (−12.7 to −0.6)
LA size z-score (Range)	3.7 (1.6 to 5)	2.8 (0.4 to 4.1)	2.8 (1.9 to 3.9)	1.9 (1.4 to 3.5)
Arrhythmia (%)	1 (16.7%)	2 (50%)	2 (50%)	2 (15.3%)
SCD (%)	1 (16.7%)	0	1 (25%)	0
ICD (%)	0	0	1 (25%)	1 (7.6%)
Transplant (%)	0	2 (50%)	0	1 (7.6%)
Deceased (%)	1 (4%)	0	2 (50%)	0

NYHA = New York Heart Association functional class; LVMWT = Left Ventricular Maximal Wall Thickness; LVEDD = Left Ventricular End Diastolic Dimension; FS=Fractional Shortening; LA = Left Atrium; SCD = Sudden Cardiac Death; ICD = Implantable Cardiac Defibrillator.