Fig. 11.

XX DSD, ovotesticular. ACS with bilateral ovotestes. a A prepuce-like vulva is present and the enlarged clitoris, which contains a bone, protrudes from the vulva. b Ovotestis. The cortex has several stages of ovarian follicles containing oocytes and regressing corpora lutea. The medulla contains Leydig cells in the interstitium and seminiferous tubules containing Sertoli cells only, as in XX males (see fig. 10b) (reprinted with permission from Cold Spring Harbor Laboratory Press: Meyers-Wallen [2006]).