XY DSD, ovotesticular. a External genitalia of a cat affected with ovotesticular DSD. The cat is in standing position, such that the nonpigmented anus is dorsal, the penis is ventral, and the scrotum, which does not contain testes, is between the anus and penis. Hair surrounding the scrotum and prepuce is pigmented. b Bilateral ovotestes were present. A band of connective tissue separated the smaller cortical rim of ovarian tissue from the larger medullary testis. Rare primordial follicles and oocytes were observed. The central medullary region contained Leydig cells, small irregular sex cords and hypoplastic seminiferous tubules lined by Sertoli cells (reprinted with permission from Veterinary Pathology: Schlafer et al. [2011]).