Table 1.
DM1 (n=622) | Congenital and childhood DM1 (n=86) | DM2 (n=117) | FSHD (n=574) | |
---|---|---|---|---|
Mean (±standard deviation) | ||||
Enrollment age (yrs) | 43.5 (12.1) | 12.8 (9.9) | 54.3 (12.4) | 46.1 (15.9) |
Age at onset (yrs) | 25.9 (13.0) | 3.3 (4.9) | 33.5 (13.9) | 21.5 (15.0) |
Body Mass Index (kg/m2) | 25.2 (5.6) | 19.6 (6.0) | 26.9 (5.2) | 24.9 (5.6) |
% (n) | ||||
Female | 51.1% (318) | 43.0% (37) | 66.7% (78) | 52.3% (300) |
Genetically confirmed | 51.4% (320) | 68.6% (59) | 58.1% (68) | 59.1% (339) |
Racial categories | ||||
Asian | 0.5% (3) | 3.5% (3) | 0.9% (1) | 2.4% (14) |
American Indian/Alaska Native | 0.6% (4) | 0% (0) | 0.9% (1) | 1.1% (6) |
Black or African American | 0.6% (4) | 1.2% (1) | 0 (0%) | 0.7% (4) |
Native Hawaiian or Other Pacific Islander | 0.2% (1) | 0% (0) | 0% (0) | 0% (0) |
White | 95.2% (592) | 89.5% (77) | 97.4% (114) | 93.4% (536) |
Not reported | 2.9% (18) | 5.8% (5) | 0.9% (1) | 2.4% (14) |
% (n) | ||||
Ethnicity | ||||
Hispanic | 4.5% (28) | 4.7% (4) | 0.9% (1) | 3.3% (19) |