Figure 2.

Fundus photographs of affected individuals from both families and of a normal individual. A, B: Right and left fundus, respectively, of the proband of family A (see arrow, Figure 1A), representative of the fundus appearance of all affected members of this family. Arrows indicate yellow perifoveal annular rings. C, D: Right and left fundus, respectively, of the proband of family B (see arrow, Figure 1B). Arrowheads point to the developing perifoveal annular rings. E, F: Right and left fundus, respectively, of a normal individual.