Table 1. Comparison of ERG responses of affected individuals of families A and B with a control individual.
| Measured parameters using monopolar electrodes | Adaptation | Flash strength (cds/m2) | Proband Family A | Proband Family B | Control | Normal values (Age=20 years) |
|---|---|---|---|---|---|---|
| Scotopic 25 dB b-wave amplitude (µV) |
Dark |
0.01 |
13.3 |
21.8 |
244.4 |
>185 |
| Scotopic 0 dB b-wave amplitude (µV) |
Dark |
3 |
22.7 |
22.2 |
650 |
>419 |
| Oscillatory potential amplitude (µV) |
Dark |
3 |
56.4 |
47.9 |
187.7 |
>110 |
| Photopic 0 dB b-wave amplitude (µV) |
Light |
3 |
12 |
15.7 |
86.9 |
>102 |
| Photopic 30 Hz flicker amplitude (µV) | Light | 3 | 6.1 | 1.46 | 65.6 | >70 |
Age of affected individuals from families A and B at the time of investigation was 20 years.