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. 2012 Jun 1;185(11):1154–1165. doi: 10.1164/rccm.201111-2082CI

TABLE 1.

INCIDENCE OF PULMONARY HYPERTENSION AMONG DIFFERENT TYPES OF HEMOLYTIC ANEMIA

Hemolytic Anemia Type Incidence References
Hemoglobin SS disease Increased 9, 73
Hemoglobin SC disease Increased 73, 76
Hemoglobin SOArab disease Increased 73
Hemoglobin Sβ+ disease Increased 73, 76, 98
Hemoglobin Sβ0 disease Increased 73
β-Thalassemia major Increased 99101
β-Thalassemia intermedia Increased 102, 103
Hemoglobin E/β-thalassemia Increased 104
G6PD deficiency Not reported
Hereditary elliptocytosis Not reported
Hereditary ovalocytosis Not reported
Hereditary spherocytosis Increased 105
Idiopathic autoimmune Reported 106, 107
Microangiopathic Reported 108, 109
Paroxysmal nocturnal hemoglobinuria Increased 110, 111
Malaria Reported 112