Table 2.
Further definition of the underlying NCFB etiologies
Postinfectious (84) | TB (37), MAC (5), Pertussis (3), Invasive Aspergillosis (2), Measles (1), Diphtheria (1), Blastocystes hominis (1), unkown (34) |
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COPD (64) | GOLD II (10), GOLD III (28), GOLD IV (26) |
Interstitial lung disease (57) | EAA (15), IPF/NSIP (27), BOOP (9), drug induced ILD (3), UIP (3) |
Rheumatic lung disease RA (29), Sjögren (5), Sclerodermia (4), AS (1), MCTD (1) (40) | |
Immunodeficiency (29) | CVID (1), HIV (1), hyper IgE syndrome (1), other immunoglobulin deficits (14 dysgammaglobulinemia, 1 agammaglobulinemia, 2 hypogamma-globulinemia), Navajo poikiloderma (1), different types of post transplants (5) (3 kidney, 1 liver and 1 heart), non-thoracic Non-Hodgkin lymphoma (2), chronic lymphatic leukemia (1) |
Thoracic cancer (38) | adenocarcinoma (9), large cell anaplastic carcinoma (1), squamous cell carcinoma (16), small-cell lung carcinoma (3), thoracic Non-Hodgkin lymphoma (3), carcinoid (1), mesothelioma (2), solitary pulmonary nodule without tissue diagnosis (3) |
Other causes (44) | sarcoidosis (13), anatomic malformations (6), UC (6), Crohn (3), SJM (3), aspiration/inhalation (3), α1-ATD (2), CS vasculitis (2), Wegener (2), MK (1), PE (1), WC (1), Microscopic polyangiitis (1) |
The number in brackets states the number of patients. AS = Ankylosing Spondylitis, α1-ATD = alfa-1-antitrypsin deficiency, BOOP = Bronchiolitis Obliterans Organizing Pneumonia, COPD = Chronic Obstructive Lung Disease, CS = Churg-Strauss, CVID = Common Variable Immunodeficiency, EAA = Extrinsic Allergic Alveolitis, ILD = Interstitial Lung Disease, IPF = Idiopathic Pulmonary Fibrosis, MAC = Mycobacterium avium complex, MCTD = Mixed Connective Tissue Disease, MK = Mounier-Kuhn Syndrome, NSIP = Nonspecific Interstitial Pneumonia, PE = Pseudoxanthoma Elasticum, RA = Rheumatoid Arthritis, SJM = Swyer-James-McLeod Syndrome, TB = Tuberculosis, UC = Ulcerative Colitis, UIP = Usual Interstitial Pneumonia, WC = Williams-Campbell syndrome