Table 3.
Haematological features of different types of haemoglobinopathies in the study subjects.
| Variable | Normal | β-thalassemia minor | E-β-thalassemia | E-disease | E-trait | β-thalassemia major | δ-β-Thalassemia | D/S Trait | P value (for overall difference) |
|---|---|---|---|---|---|---|---|---|---|
| N | 253 | 128 | 81 | 65 | 73 | 3 | 3 | 4 | |
| Hb (g/dL) | 12.3 ± 2.96 | 9.23 ± 2.06 | 6.12 ± 1.61 | 7.65 ± 3.76 | 10.9 ± 3.76 | 5.26 ± 1.30 | 11.3 ± 1.69 | 9.97 ± 5.00 | <0.001 |
| Hb A (%) | 75.9 ± 17.7 | 60.4 ± 14.6 | 12.6 ± 5.32 | 2.39 ± 0.83 | 2.39 ± 0.84 | 12.2 ± 2.98 | 87.5 ± 3.32 | 53.1 ± 13.2 | <0.001 |
| Hb A2 (%) | 2.02 ± 1.06 | 3.13 ± 1.26 | — | — | — | — | 2.70 ± 0.84 | 1.62 ± 0.21 | <0.001 |
| Hb E (%) | — | 0.73 ± 0.07 | 45.6 ± 13.9 | 27.1 ± 4.41 | 30.2 ± 11.2 | — | — | 18.9 ± 7.72 | <0.001 |
| Hb F (%) | — | 3.68 ± 1.35 | 41.5 ± 14.8 | 3.84 ± 1.60 | 0.15 ± 0.04 | 85.6 ± 3.75 | 9.75 ± 2.41 | 26.2 ± 7.32 | <0.001 |
| RBC (106/μL) | 4.51 ± 0.84 | 4.77 ± 1.17 | 3.44 ± 0.87 | 3.92 ± 1.06 | 4.77 ± 0.67 | 2.80 ± 0.63 | 3.63 ± 0.12 | 4.49 ± 1.05 | <0.001 |
| HCT (%) | 37.5 ± 7.82 | 30.7 ± 6.18 | 22.1 ± 5.08 | 24.9 ± 6.52 | 32.6 ± 4.73 | 18.6 ± 5.50 | 34.2 ± 1.97 | 31.4 ± 11.4 | <0.001 |
| MCV (fl) | 79.4 ± 11.9 | 64.7 ± 12.4 | 64.8 ± 7.13 | 64.2 ± 7.37 | 68.7 ± 7.26 | 65.7 ± 4.85 | 82.0 ± 8.69 | 69.2 ± 13.8 | <0.001 |
| MCH (pg) | 23.2 ± 6.12 | 19.5 ± 3.31 | 17.8 ± 2.13 | 18.3 ± 2.95 | 21.3 ± 3.17 | 18.7 ± 0.61 | 26.3 ± 1.20 | 21.6 ± 6.98 | <0.001 |
| MCHC (g/dL) | 29.7 ± 5.40 | 31.7 ± 8.15 | 27.5 ± 2.25 | 28.6 ± 3.63 | 30.9 ± 2.57 | 28.5 ± 1.55 | 32.2 ± 1.97 | 30.6 ± 4.35 | >0.05 |
Data are mean ± SD.