Table 1.
Demographic information.
| Participant | Sex | Age of ID (yrs;mos) | Etiology | Age at visit (mos) | Age at first CI (mos) | Hearing Age (mos) | Age at second CI (mos) | Duration of BICI (mos) | First CI (Internal device, processor, ear) | First CI Speech processing strategy | Second CI (Internal device, processor, ear) | Second CI Speech processing strategy |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
|
BICI group CIBV |
M | birth | Connexins 26, 30 | 29 | 17 | 12 | 23.5 | 5.5 | HiRes, PSP, R | HiRes-S | HiRes, PSP, L | HiRes-S |
| CIBX | M | birth | Waardenburg Syndrome | 31.5 | 10 | 21.5 | 12 | 19.5 | N24, Sprint, R | ACE | N24, Sprint, L | ACE |
| CICA | M | 2;0 | Unknown | 35 | 29 | 6 | 29 | 6 | Pulsar, Tempo, simultaneous | CIS+ | Pulsar, Tempo, simultaneous | CIS+ |
| CICB | F | birth | Connexin 26 | 31 | 10.5 | 20.5 | 25 | 6 | N24, Sprint, R | ACE | Freedom, Freedom, L | ACE (RE) |
| CICF | F | 2;0 | Meningitis^ | 34.5 | 18 | 16.5 | 28.5 | 6 | Freedom, Freedom, R | ACE | Freedom, Freedom, L | ACE |
| CICG | M | birth | Connexin 26 | 27 | 13 | 14 | 20.5 | 6.5 | C40+, Tempo, R β | CIS+ | Pulsar, Tempo, L β | CIS+ |
| CICH | M | birth | Unknown | 27 | 12 | 15 | 12 | 15 | Pulsar, Tempo, R β | CIS+ | Pulsar, Tempo, L β | CIS+ |
| CICK | M | 0;11 | Connexin 26 | 28.5 | 13 | 15.5 | 15.5 | 13 | HiRes, PSP, R | HiRes P | HiRes, PSP, L | HiRes-P |
| CICO | M | birth | Connexin 26 | 31 | 14 | 17 | 25.5 | 5.5 | Freedom, Freedom, R | ACE (RE) | Freedom, Freedom, L | ACE (RE) |
| CICP | F | birth | Connexin 26 | 26.5 | 13 | 13.5 | 20 | 6.5 | Freedom, Freedom, R | ** | Freedom, Freedom, L | ** |
| CICR | M | birth | Connexin 26 | 26 | 12.5 | 13.5 | 16.5 | 9.5 | HiRes, PSP, L | HiRes-P w/ Fidelity 120 | HiRes, PSP, R | HiRes-P w/ Fidelity 120 |
| CICS | M | 0;10 | Connexin 26 | 34.5 | 18 | 16.5 | 18 | 16.5 | HiRes, Harmony, simultaneous | HiRes-P w/ Fidelity 120 | HiRes, Harmony, simultaneous | HiRes-P w/ Fidelity 120 |
| CICT | M | birth | Connexin 26 | 35 | 11.5 | 23.5 | 22.5 | 12.5 | HiRes, PSP, R | HiRes-P w/ Fidelity 120 | HiRes, PSP, L | HiRes-P w/ Fidelity 120 |
| CICU | F | birth | Unknown^* | 31 | 15 | 16 | 24 | 7 | Freedom, Freedom, L | ACE | Freedom, Freedom, R | ACE |
| CICV | M | birth | Connexin 26 | 33.5 | 12 | 21.5 | 26 | 7.5 | HiRes, Harmony, R (T-mic) | HiRes-P w/ Fidelity 120 | HiRes, Harmony, L (T-mic) | HiRes-P w/ Fidelity 120 |
| CICW | F | 0;1 | Unknown | 29 | 14 | 15 | 15 | 14 | Pulsar, Tempo, R β | CIS+ | Pulsar, Tempo, L β | CIS+ |
| CICX | F | birth | Unknown | 36 | 20.5 | 15.5 | 27.5 | 8.5 | Freedom, Freedom, R | ACE | Freedom, Freedom, L | ACE |
| CIDA | F | birth | Connexin 26 | 34.5 | 11 | 23.5 | 22 | 12.5 | HiRes, PSP, R | HiRes-P w/ Fidelity 120 | HiRes, PSP, L | HiRes-P w/ Fidelity 120 |
| CIDC | M | birth | Unknown^* | 31 | 18 | 13 | 18 | 13 | HiRes, Auria, L | HiRes-S | HiRes, PSP, R | HiRes-S |
| CIDD | F | 1;1 | Unknown | 36 | 21 | 15 | 29 | 7 | Freedom, Freedom, L | ACE | Freedom, Freedom, R | ACE |
| CIDE | M | birth | Unknown | 26.5 | 13 | 13.5 | 13 | 13.5 | HiRes, PSP, simultaneous | HiRes-P | HiRes, PSP, simultaneous | HiRes-P |
| CIDH | M | 0:10 | Unknown | 35.5 | 17 | 18.5 | 26 | 9.5 | Freedom, Freedom, R | ACE | Freedom, Freedom, L | ACE |
| CIDI | M | birth | Connexin 26 | 26 | 8 | 18 | 9 | 17 | Pulsar, Tempo, L β | CIS+ | Pulsar, Tempo, R β | CIS+ |
| CIDK | M | birth | Connexin 26 | 26.5 | 9.5 | 17 | 9.5 | 17 | Freedom, Freedom, simultaneous | ACE | Freedom, Freedom, simultaneous | ACE |
| CIDL | F | birth | Connexin 26 | 27.5 | 14 | 13.5 | 18 | 9.5 | Pulsar, Tempo, R β | CIS+ | Sonata, Tempo, L β | CIS+ |
| CIDM | F | birth | Unknown | 31.5 | 13 | 18.5 | 25 | 6.5 | HiRes, Harmony, L | HiRes-P w/ Fidelity 120 | HiRes, Harmony, R | HiRes-P w/ Fidelity 120 |
| CIEA | M | birth | Connexin 26 | 28 | 8 | 20 | 11 | 17 | Freedom, Freedom, R | ACE (RE) | Freedom, Freedom, L | ACE (RE) |
|
UCI group CICC |
M | birth | Familial (hereditary) | 36 | 15 | 21 | N24, Sprint, L | ACE | ||||
| CICE | M | birth | Connexins 26, 30 | 30 | 10.5 | 19.5 | HiRes, Auria, R | HiRes-P | HA | |||
| CICI | M | birth | Unknown | 36 | 14.5 | 21.5 | Pulsar, Tempo+, R | CIS+ | ||||
| CICJ | M | birth | Connexin 26 | 35 | 10 | 25 | HiRes, R | HiRes-P | ||||
| CICL | M | 1;1 | Connexin 26* | 27 | 16 | 11 | Freedom, Freedom, R | ACE (RE) | ||||
| CICM | M | birth | Connexin 26 | 36 | 13 | 23 | HiRes, PSP, R | ** | ||||
| CICN | F | birth | Connexin 26 | 32.5 | 15.5 | 17 | Freedom, Freedom, R | ACE (RE) | ||||
| CICQ | M | 0;8 | Usher Syndrome Type 1 | 31 | 14.5 | 16.5 | Freedom, Freedom, R | ACE | ||||
| CICZ | F | 0;2 | Unknown | 31 | 7 | 24 | HiRes, PSP, R | HiRes-P w/ Fidelity 120 | HA | |||
| CIDB | F | 0;11 | CMV^ | 35 | 16 | 19 | HiRes, PSP, R | HiRes-P w/ Fidelity 120 | HA | |||
| CIDS | M | 0;3 | Unknown | 25 | 12.5 | 12.5 | Freedom, Freedom, R | ACE | ||||
| CIDU | F | birth | Unknown | 28.5 | 13 | 15.5 | HiRes, Auria, R | HiRes-P |
ID refers to identification. Carets (^) represent children who have a history of acoustic hearing. Asterisks (*) represent children who have a history of progressive hearing loss per parental report. Betas (β) represent children who use implant processors with a body-level microphone. Double asterisks (**) refer to unknown speech processing strategies for respective participants. The abbreviation “HA” reflects children who use a hearing aid in the non-implanted ear either consistently (CICE, CICZ) or intermittently (CIDB). Cochlear implant devices: N24, Freedom (Cochlear Corp.); HiRes (Advanced Bionics); Pulsar, C40+, Sonata (MED-EL Corp.)