Table 1.

Example menus comparing a daily diet containing amino acid-based formula or GMP products.^a,^b

	AA Diet				GMP Diet
Breakfast	Amount	Phe (mg)	Protein (g)	Breakfast	Amount	Phe (mg)	Protein (g)
Phenex 2® c	100 g powder	0	30	GMP Bettermilk®c	50 g powder	23	15
Cheerios® cereal	1 cup (28 g)	165	3.2	GMP Crisp cereal	1 1/2 c (66 g)	30	10
Subtotal, Breakfast		165	33.2	Subtotal, Breakfast		53	25
Lunch				Lunch
				GMP sports beverage	12 oz	11	8
White bread, LPd	2 slices (100 g)	9	0.2	White bread, LPd	2 slices (100 g)	9	0.2
Cheese, LP	2 slices (40 g)	42	0.8	Cheese, LP	2 slices (40 g)	42	0.8
Mayonnaise	1 Tbsp (13 g)	8	0.2	Mayonnaise	1 Tbsp (13 g)	8	0.2
Grapes, green	20	19	0.7	Grapes, green	20	19	0.7
Apple juice	8 oz (240 ml)	2	0
Subtotal, Lunch		80	1.9	Subtotal, Lunch		89	9.9
Snack				Snack
				GMP snack bar	1 bar (84 g)	28	15
Soda, regular	12 oz (360 ml)	0	0	Soda, regular	12 oz (360 ml)	0	0
Chips, Doritos®	30 g	97	2.0
Subtotal, Snack		97	2.0	Subtotal, Snack		28	15
Dinner				Dinner
				GMP sports drink	8 oz (240 ml)	8	5
Spaghetti, LP	1.5 c. cooked (56 g dry)	7	0.3	Spaghetti, LP	1.5 c cooked (56 g dry)	7	0.3
Spaghetti sauce, no meat	1 c (230 g)	92	3.7	Spaghetti sauce, no meat	1 c (230 g)	92	3.7
Carrot sticks	60 g	37	0.6	Carrot sticks	60 g	37	0.6
Italian salad dressing	1 oz (30 ml)	0	0	GMP salad dressing	1 oz (30 ml)	15	5
Apple juice	12 oz (360 ml)	3	0.2
Subtotal, Dinner		139	4.8	Subtotal, Dinner		159	14.6
Snack				Snack
Phenex 2®	67 g, powder	0	20	GMP strawberry pudding	1 c (255 g)	37	15
Amino Acid Blend®	20 g	0	15	Chips, Doritos®	30 g	97	2.0
Subtotal, Snack		0	35	Subtotal, Snack		134	17
TOTAL		481	76.9	TOTAL		463	81.5

^aDiets designed for a 12 year old female with classical PKU; weight = 42 kg, height = 152 cm. Her phe tolerance is 460–480 mg/day, minimum protein needs of 1.0 g/kg = 42 g/day and daily energy needs of 2300–2400 kcals.

^bTotal energy content of AA Diet = 2365 kcals (565 kjoules) and GMP Diet = 2325 kcals (556 kjoules).

^cGMP and amino acid based medical foods are in bold. Commercial products include Phenex 2® (Abbott Nutrition, Columbus OH), PKU Amino Acid Blend® (Applied Nutrition, Cedar Knolls NJ) and Bettermilk® (Cambrooke Foods, Boston MA). Composition of other GMP products is based on estimates provided by Cambrooke Foods in April 2011.

^dLP = low protein product made from wheat starch.