Table 1.
AA Diet | GMP Diet | ||||||
---|---|---|---|---|---|---|---|
| |||||||
Breakfast | Amount | Phe (mg) | Protein (g) | Breakfast | Amount | Phe (mg) | Protein (g) |
Phenex 2® c | 100 g powder | 0 | 30 | GMP Bettermilk®c | 50 g powder | 23 | 15 |
Cheerios® cereal | 1 cup (28 g) | 165 | 3.2 | GMP Crisp cereal | 1 1/2 c (66 g) | 30 | 10 |
| |||||||
Subtotal, Breakfast | 165 | 33.2 | Subtotal, Breakfast | 53 | 25 | ||
| |||||||
Lunch | Lunch | ||||||
GMP sports beverage | 12 oz | 11 | 8 | ||||
White bread, LPd | 2 slices (100 g) | 9 | 0.2 | White bread, LPd | 2 slices (100 g) | 9 | 0.2 |
Cheese, LP | 2 slices (40 g) | 42 | 0.8 | Cheese, LP | 2 slices (40 g) | 42 | 0.8 |
Mayonnaise | 1 Tbsp (13 g) | 8 | 0.2 | Mayonnaise | 1 Tbsp (13 g) | 8 | 0.2 |
Grapes, green | 20 | 19 | 0.7 | Grapes, green | 20 | 19 | 0.7 |
Apple juice | 8 oz (240 ml) | 2 | 0 | ||||
| |||||||
Subtotal, Lunch | 80 | 1.9 | Subtotal, Lunch | 89 | 9.9 | ||
| |||||||
Snack | Snack | ||||||
GMP snack bar | 1 bar (84 g) | 28 | 15 | ||||
Soda, regular | 12 oz (360 ml) | 0 | 0 | Soda, regular | 12 oz (360 ml) | 0 | 0 |
Chips, Doritos® | 30 g | 97 | 2.0 | ||||
| |||||||
Subtotal, Snack | 97 | 2.0 | Subtotal, Snack | 28 | 15 | ||
| |||||||
Dinner | Dinner | ||||||
GMP sports drink | 8 oz (240 ml) | 8 | 5 | ||||
Spaghetti, LP | 1.5 c. cooked (56 g dry) | 7 | 0.3 | Spaghetti, LP | 1.5 c cooked (56 g dry) | 7 | 0.3 |
Spaghetti sauce, no meat | 1 c (230 g) | 92 | 3.7 | Spaghetti sauce, no meat | 1 c (230 g) | 92 | 3.7 |
Carrot sticks | 60 g | 37 | 0.6 | Carrot sticks | 60 g | 37 | 0.6 |
Italian salad dressing | 1 oz (30 ml) | 0 | 0 | GMP salad dressing | 1 oz (30 ml) | 15 | 5 |
Apple juice | 12 oz (360 ml) | 3 | 0.2 | ||||
| |||||||
Subtotal, Dinner | 139 | 4.8 | Subtotal, Dinner | 159 | 14.6 | ||
| |||||||
Snack | Snack | ||||||
Phenex 2® | 67 g, powder | 0 | 20 | GMP strawberry pudding | 1 c (255 g) | 37 | 15 |
Amino Acid Blend® | 20 g | 0 | 15 | Chips, Doritos® | 30 g | 97 | 2.0 |
| |||||||
Subtotal, Snack | 0 | 35 | Subtotal, Snack | 134 | 17 | ||
| |||||||
TOTAL | 481 | 76.9 | TOTAL | 463 | 81.5 |
Diets designed for a 12 year old female with classical PKU; weight = 42 kg, height = 152 cm. Her phe tolerance is 460–480 mg/day, minimum protein needs of 1.0 g/kg = 42 g/day and daily energy needs of 2300–2400 kcals.
Total energy content of AA Diet = 2365 kcals (565 kjoules) and GMP Diet = 2325 kcals (556 kjoules).
GMP and amino acid based medical foods are in bold. Commercial products include Phenex 2® (Abbott Nutrition, Columbus OH), PKU Amino Acid Blend® (Applied Nutrition, Cedar Knolls NJ) and Bettermilk® (Cambrooke Foods, Boston MA). Composition of other GMP products is based on estimates provided by Cambrooke Foods in April 2011.
LP = low protein product made from wheat starch.