Table 1. Demographics and tomographic features of patients with pseudoxanthoma elasticum.
| Demographics | |
|---|---|
| Number | 52 eyes (27 patients) |
| Men/women | 17/10 (62.9%/37.1%) |
| Age (years)a | 65.8 (10.1) (range, 50–89) |
| Follow-up period (months)a | 39.5 (18.8) (range, 3–61) |
| SD-OCT follow-up period (months)a | 12.6 (9.6) (range, 1–27) |
| Results of skin biopsy, patient number (%)b | 26 (96.3%) PXE positive(biopsy was not done for one patient) |
| Refractiona | −1.3 (2.05) (−6.5 to 1.5) |
| Log MAR BCVA at first SD-OCT visita | 0.68 (0.54) (range, −1.8 to 1.6) |
| Change in log MAR BCVAa | 0.19 (0.36) (range, −0.33 to 1.3) |
| Secondary CNVb | 44 eyes (84.6%) |
| Tomographic features | |
| ORT (%)b | 31 (59.6%) |
| Location of ORT | |
| On border of CNV | 23 (74.2%) |
| Over CNV | 12 (38.7%) |
| Cystoid spacesb | 23 (44.2%) |
| Bruch's membrane undulation (%)b | 38 (73.1%) |
| SRD (%)b | 7 (13.5%) |
Abbreviations: AS, angioid streaks; BCVA, best-corrected visual acuity; CNV, choroidal neovascularization; Log MAR, logarithm of the minimal angle of resolution; ORT, outer retinal tubulation; PXE, pseudoxanthoma elasticum; SRD, serous retinal detachment; SD-OCT, spectral-domain optical coherence tomography.
a
Values are expressed as means (SD), with the range shown in adjacent parentheses.
b
Values are the number of eyes, with percentage shown in parenthesis.