Table 3.
Case | CNV # | CS | CI | CI/CS | CII/CIII | CII/CIII/CS | CIV | CIV/CS |
---|---|---|---|---|---|---|---|---|
1 | 2 | 930 | 89.4 | 96.1 | 155 | 167 | 0.68 | 0.73 |
2 | 13 | 1746 | 62.8 | 36.0 | 571 | 327 | 1.06 | 0.61 |
CS = citrate synthase activity: CI, CII, CIII, and CIV–OXPHOS complexes I–IV. Specific activities presented as nmole/min/mg protein