Table 1.
Clinical features of GT and PEG-ADA treated patients at the time of analysis
Patients | Age, y | Follow-up, y | Autoimmunity | T cells, counts/μL |
dAXP, μmol | |
---|---|---|---|---|---|---|
CD3 | CD4 | |||||
GT (n = 11) | 4.5 (1.5-10.8) | 3 (1-8.5) | 1 patient with hypothyroidism | 848 (452-2911) | 410 (121-709) | 15 (0-84) |
PEG-ADA (n = 7) | 12.1 (0.6-23) | 13 (0.5-21.2) | 1 patient with type I diabetes | 1489 (71-4599) | 671 (35-1653) | 4 (0-74) |
Data are median (range).
dAXP indicates deoxyadenosine nucleotides in RBCs.