Table 1.
Classification of cutaneous forms of mastocytosis (adapted from [10])
| Maculopapular cutaneous mastocytosis/Urticaria pigmentosa |
| Subvariants: Typical urticaria pigmentosa |
| Plaque-form |
| Nodular |
| Telangiectasia macularis eruptiva perstans (TMEP) |
| Diffuse cutaneous mastocytosis |
| Mastocytoma of skin |