Table 1.
Classification of cutaneous forms of mastocytosis (adapted from [10])
Maculopapular cutaneous mastocytosis/Urticaria pigmentosa |
Subvariants: Typical urticaria pigmentosa |
Plaque-form |
Nodular |
Telangiectasia macularis eruptiva perstans (TMEP) |
Diffuse cutaneous mastocytosis |
Mastocytoma of skin |