Table 2.
WHO Classification of mastocytosis (adapted from [10])
| Cutaneous mastocytosis (CM) |
| Indolent systemic mastocytosis (ISM) |
| Subvariants: Isolated bone marrow mastocytosis |
| Smouldering systemic mastocytosis |
| Systemic mastocytosis with an associated clonal hematologic non-mast-cell lineage disease (SM-AHNMD) |
| Aggressive systemic mastocytosis |
| Subvariant: Lymphadenopathic mastocytosis with eosinophilia |
| Mast cell leukemia |
| Mast cell sarcoma |
| Extracutaneous mastocytoma |