TABLE 2.
Clinical Characteristics of Fontan Group (N = 54)
| Characteristics | n | % |
|---|---|---|
| Single ventricle diagnosis | ||
| Tricuspid atresia | 19 | 35 |
| Double inlet left ventricle | 13 | 24 |
| Hypoplastic RV | 8 | 15 |
| HLHS/Variants | 4 | 7 |
| Double outlet right ventricle | 3 | 6 |
| Atrioventricular canal | 2 | 4 |
| Ebstein anomaly | 1 | 2 |
| Other complex anatomy | 4 | 7 |
| Ventricle type | ||
| Left | 42 | 78 |
| Right | 9 | 17 |
| Undetermined | 3 | 5 |
| Fontan type | ||
| Classic RA to PA | 15 | 28 |
| Bjork RA to RV | 2 | 4 |
| Lateral tunnel | 24 | 44 |
| Extracardiac Fontan | 13 | 24 |
| Fontan revision | ||
| Yes | 18 | 33 |
| Fontan fenestration | ||
| Yes | 20 | 33 |
| Number daily medications | ||
| ≥3 | 33 | 61 |
| <3 | 21 | 39 |
| NYHA classification | ||
| I | 26 | 48 |
| II | 17 | 32 |
| III | 11 | 20 |
| LVEF% | ||
| ≤50 | 14 | 33 |
| >50 | 28 | 67 |
| History of arrhythmias | ||
| Yes | 41 | 76 |
| Pacemaker | ||
| Yes | 22 | 41 |
| Oxygen saturation | ||
| ≤90 | 17 | 31 |
| >90 | 37 | 69 |
Abbreviations: HLHS, hypoplastic left ventricular heart syndrome; LVEF%, left ventricle ejection fraction; NYHA, New York Heart Association; PA, pulmonary artery; RA, right atrium; RV, right ventricle.