Table 1.
Patient details
Patient | Type of haemophilia | Virology | Year of surgery | Age at surgery | Localisation | Dimension (cm) | Symptoms | Surgery | FVIII | Remarks | Outcome |
---|---|---|---|---|---|---|---|---|---|---|---|
1 | A <1% | Not available | 1967 | 40 | Thigh R | Not available | Not available | Above knee amputation | Not available | Not available | No recurrence |
2 | A <1% | Hep C | 1984 | 43 | Iliac L | 20 x 11.5 | Growing mass over 1.5 years, no pain | Resection | Yes | Infection, fistula after 12y and 17y | No recurrence |
3 | A <1% | Hep C, B | 2000 | 40 | Iliac L | 17.5 x 10.1 | Growing mass over 1 year, pain | Resection, cement, pin | Yes | No recurrence | |
2007 | 48 | Thigh R | 9.5 x 7.2 | Growing mass over 7 months, no pain | Excision | Yes | Died, liver failure after 3 years | No recurrence | |||
4 | A <1% | Hep C | 2000 | 41 | Elbow L | 3.2 x 2 | Paraesthesia over 3 years, pain over 6 months | Resection | Yes | Inhibitor | No recurrence |
Inhibitor | Died, liver failure after 7.5 years | ||||||||||
5 | A <1% | Hep C, B | 2004 | 61 | Iliac R | 22.5 x 15 | Growing mass over 1.5 years, no pain | Resection, cement, pin | Yes | Infection after 4 weeks | No recurrence |
Died, liver failure after 5 years | |||||||||||
6 | A <1% | Hep C, B, HIV | 2000 | 48 | Tibia R | 9.6 x 3.3 | Pain over 4 months | Curettage, cement, LCDCP titanium | Yes | Infection, fistula after 5 months | No recurrence |
Hep hepatitis, R right, L left