Table 1.

Variables selected by consensus (≥80%) during second round of the Delphi survey

				CAPS
Variables	FMF (%)	TRAPS (%)	MKD (%)	FCAS (%)	MWS (%)	NOMID (%)
Fatigue		82	81	87	87	82
Number of days of illness in the past 3 months	94	88	100	93	87	82
Intensity of attacks	89		81
Arthritis	100
Arthralgia			87		80	87
Measure of joint damage						94
Presence absence of skin rash	94	81	82	100	100	88
Intensity of skin rash				93	87	88
Frequency of skin rash				87	80
Number of days with skin rash in a month				93	93	82
Chest symptoms	94
Muscle symptoms	82
Gastrointestinal symptoms		100
Painful lymphnodes			94
Hearing loss					93	82
Eye symptoms						82
Headaches						82
Brain MRI						82
Cognitive function test						94
Funduscopy						88
Limitation of daily activity	89		87	87	80	81
Days of school /work loss	83		81
Global DAS physician	83		81			88
Global DAS patient						82
ESR	83

New variables/items suggested by experts after the first round are shown in italics.

CAPS, cryopyrin-associated periodic syndromes; CINCA/NOMID, chronic infantile neurological, cutaneous, articular/neonatal onset multisystem inflammatory disease; DAS, Disease Activity Score; ESR, erythrocyte sedimentation rate; FCAS, familial cold autoinflammatory syndrome; FMF, familial Mediterranean fever; MKD, mevalonate kinase deficiency; MWS, Muckle-Wells syndrome; TRAPS, TNF receptor-1-associated periodic syndrome.