Table 1.
Patients with KHE without cutaneous involvement.
| Age of Presentation |
Presenting Symptoms | Depth of Infiltration | KMP |
|---|---|---|---|
| Birth | Thrombocytopenia/congestive heart failure | Retroperitoneum | Yes |
| Birth | Petechiae/Thrombocytopenia | Retroperitoneum | Yes |
| 5 weeks | Ascites/respiratory distress | Retroperitoneum | Yes |
| 4 months* | Bloody stool | Retroperitoneum | Yes |
| 6 months | Abdominal mass/Thrombocytopenia | Retroperitoneum | Yes |
| 3 years | Abdominal pain/distention | Retroperitoneum (pancreas) | No |
| 4 months | Enlarging mass | Muscle (gluteus) | Yes |
| 7 months | Hypotonia | Muscle (paraspinal) | No |
| 10 months | Progressive lower extremity weakness | Muscle (paraspinal) | Yes |
| 2 years | Extremity pain/limp | Bone (femur) | No |
| 4 years | Hip pain/refusal to walk | Bone (sacrum) | No |
| 6 years | Back pain | Bone (vertebrae) | No |
Histopathology of all cases supported the KHE diagnosis, except one * without available histology.