Table 3.

Neuroimaging

Patient	Exams	Inner Ear	Vasculature	Comments
A1	CT brain and petrous bone	Bilateral CCD with narrow right internal auditory canal	Bilateral hypoplastic ICA; enlarged vertebrobasilar system and Pcoms
B1	MRI brain	Right: Aplasia of inner ear structures (cochlea, vestibule, and semicircular canals); absent internal auditory canal Left: CCD with narrow internal auditory canal	Hypoplastic left ICA; enlarged basilar artery	White matter volume reduction and thin corpus callosum due to periventricular leukomalacia secondary to hypoxic-ischemic insult
C1	MRI brain	Right: Aplasia of inner ear structures (cochlea, vestibule, and semicircular canals); absent internal auditory canal and vestibulocochlear nerve; facial nerve runs in an anomalous canal in the petrous bone Left : Hypoplastic cochlea with basal turn and part of the second turn present; hypoplastic vestibule and semicircular canals; normal vestibulocochlear nerve with wide internal auditory canal	Hypoplastic left ICA Enlarged left Pcom and basilar artery; absent 6th CNs bilaterally	Abducens cranial nerves not seen; oculomotor nerves visible
F1	MRI brain	Reported normal, but images not reviewed

CCD = common cavity deformity; ICA = internal carotid artery; Pcom = posterior communicating artery; CNs = cranial nerves