. Author manuscript; available in PMC: 2014 Jan 1.

Published in final edited form as: Muscle Nerve. 2012 Oct 5;47(1):23–27. doi: 10.1002/mus.23462

Table.

HBPN patients prophylactically treated with corticosteroid

Patient #	Age (y) & Gender	Age at first Attack (yr)	Family history	SEPT9 Mutation^*	Surgery type	Anesthetic	Perioperative Steroids and Immunosuppressants

14	34 F	19	Y	Y	Caesarean section	Epidural	24 hours prior to induced delivery had MPS 1000 mg
14	34 F	19	Y	Y	Caesarean section	Epidural	Postpartum IVIG 0.4 gm/kg/day × 6 days beginning post delivery day 1

18	30 F	30	Y	Y	Thyroid resection	General	PRED 60 mg/day 1 week prior to surgery
18	30 F	30	Y	Y	Thyroid resection	General	During surgery 8 mg IV DXS

19	66 M	17	N	N	Lumbar spine surgery	General	IV MPS 1000 mg day preceding, day of, and day after surgery

All SEPT9 mutations were gene duplications including the 645 base pair exon.

Abbreviations; M=male; F=female; Y=yes; N=No; DXS=Dexamethasone; MPS=Methylprednisolone; IVIG= Intravenous immunoglobulin; PRED=Oral prednisone.