Table 1.
Diagnosis of the different IP subtypes in 3 steps
| Interstitial lung diseases (n = 88) | Step 1: histology alone (pattern) | Step 2: histology + clinical information | Step 3: interdisciplinary case evaluation |
|---|---|---|---|
|
Idiopathic interstitial pneumonia or pattern* |
85 |
77 |
63 |
| IPF/Usual interstitial pneumonia (UIP) |
31 |
29 |
27 |
| Non specific interstitial pneumonia (NSIP) |
21 |
20 |
14 |
| Respiratory bronchiolitis with ILD (RBILD) |
14 |
10 |
6 |
| Desquamative interstitial pneumonia (DIP) |
3 |
3 |
3 |
| Cryptogenic organizing pneumonia (COP) |
13 |
12 |
10 |
| Acute interstitial pneumonia (AIP) |
1 |
1 |
0 |
| Lymphocytic interstitial pneumonia (LIP) |
3 |
3 |
3 |
|
Non idiopathic interstitial pneumonia |
3 |
11 |
25 |
| Hypersensitivity pneumonitis (HP) |
0 |
3 |
10 |
| Langerhans cell histiocytosis (LCH) |
3 |
7 |
7 |
| IP of other known causes or associations |
0 |
1 |
8 |
| Correctness of diagnosis (total) | 67%* | 87%* | 100% |
*p < 0.05 vs interdisciplinary case evaluation (exact Fisher test).