. Author manuscript; available in PMC: 2014 Feb 28.
Published in final edited form as: J Cyst Fibros. 2012 Aug 28;12(2):154–164. doi: 10.1016/j.jcf.2012.07.009
© 2012 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.