Table 2.
Assessment of cognitive functions of patients by using the modified BAE test, and estimation of a generalized score for estimation of general and behavioral symptoms in patients.
| Patient | BAE scorea | Questionnaires (general score)b | ||||
|---|---|---|---|---|---|---|
| Baseline | 1 year | 3 years | Baseline | 1 year | 3 years | |
| IIIA-2 | 14 | 19 | 21 | −1 | +16 | +19 |
| IIIA-4 | 0 | 4 | 4 | +4 | +21 | +5 |
| IIIA-5 | 11 | 17 | 19 | −10 | +22 | +23 |
| IIIA-6 | 25 | 29 | 25 | 0 | +13 | +8 |
| IIIA-7 | 38 | 38 | 38 | −1 | +8 | +7 |
| IIIA-8 | 2 | 4 | 2 | −3 | +14 | +15 |
| IIIB-2 | 33 | 36 | 32 | −4 | +6 | +13 |
| IIIB-5 | 27 | 32 | 32 | −16 | +26 | +29 |
a
For information about calculation of the BAE score, see Appendix;
b
General score was calculate by summing all answers given by parents to 18 questions included in the questionnaire (for details see Table 3), giving following weights to particular types of answers: (−2) considerably deteriorated, (−1) somewhat deteriorated, (0) no changes, (+1) somewhat improved, (+2) considerably improved.