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. 2012 Dec 5;32(49):17775–17787. doi: 10.1523/JNEUROSCI.3049-12.2012

Figure 7.

Figure 7.

CMA is impaired in hSYNA53T mice, not in hSYNA53T/GFAP-Nrf2 double transgenic mice. A, Western blotting for MEF2D from total spinal cord lysates in 6-month-old hSYNA53T mice and age-match littermates. Mean ± SEM; n = 3. *p < 0.05, AN(+/−)* versus AN(−/−); #p < 0.01, AN(+/+), AN(−/+) versus AN(+/−)*. B, Fluorescent immunostaining for red, MEF2D; green, β-III tubulin; and blue, Hoechst; n = 3. Scale bar, 20 μm. C, Western blotting for CMA-related chaperone molecular HSC70, lysosomal membrane protein Lamp2a, Lamp1, and lysosomal hydrolase CatD. D, The quantified data for Lamp1, mature CatD (M). Pre, premature CatD. Mean ± SEM; n = 3. *p < 0.001, AN(+/−)* versus AN(−/−); #p < 0.001, AN(+/+), AN(−/+) versus AN(+/−)*.