Table 2. Clinicogenetic classification (consensus 2010)².

Non-syndromic ichthyoses

1. Common ichthyoses

2. ARCI

3. KI

4. Other forms of non-syndromic ichthyosis

Syndromic ichthyoses

5. X-linked ichthyosis syndromes

6. Other ichthyosis syndromes (CNS signs, fatal disease course, hair abnormalities and/or other associated signs)

Abbreviations: ARCI, autosomal recessive congenital ichthyosis; CNS, central nervous system; KI, keratinopathic ichthyoses.