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Extracellular metabolism of glucosylceramide (GlcCer) and formation of the lipid-bound envelope (LBE) (modified after ref. 260). PM: plasma membrane, Cer: ceramide, consisting of sphingosine (black) and long-chain ω-hydroxyl fatty acid (blue). Linoleic acid (green) is found esterified to the ω-hydroxyl moiety. Catabolic blocks in β-glucocerebrosidase- and SAP-C deficiency are indicated by the arrows with slashes through them.
