Table 1.
Clinical and imaging data of the patients
| Patient | Age (y)/ gender |
Duration of epilepsy (y) |
FSIQ | Fine motor function T scores |
Affected brain region |
|---|---|---|---|---|---|
| 1 | 4.3/M | 3.9 | 75 | 29 | 1FTPO |
| 2 | 8.9/M | 7.1 | 76 | 10 | rTPO |
| 3 | 11,3/F | 9.6 | 57 | 1 | rP |
| 4 | 12.4/M | 10 | 47 | −9 | rFTPO |
| 5 | 7/M | 6.5 | 47 | −65* | 1FTPO |
| 6 | 3/F | 2.2 | 128 | 36 | rP |
| 7 | 8.9/M | 8.6 | 82 | −65* | 1T(P)0 |
| 8 | 8.1/F | 7.9 | 55 | −65* | 1FTPO |
| 9 | 6/F | 5.7 | 60 | −64 | 1FTPO |
| 10 | 4.5/F | 2.5 | 91 | 35 | 1(T)P |
| 11 | 9.5/F | 8.6 | 60 | −65* | rFTPO |
| 12 | 6.3/M | 5.6 | 55 | 46 | rFTPO |
| 13 | 4.1/F | 3.6 | 102 | 34 | 1Tt |
| 14 | 3.6/F | NA | 112 | 75 | 1Tt |
| 15 | 9.5/M | 8.9 | 93 | 23 | 1P |
*
Fine motor function could not be assessed because of severe motor impairment in four subjects; the lowest score minus 1 (−65) was assigned to them; only scores measured contralateral to the brain involvement are listed.
t
These patients did not have leptomeningeal angioma; however, glucose PET showed left temporal hypometabolism and left facial angioma; intracranial involvement was further confirmed by the presence of clinical seizures or epileptiform discharges on scalp EEG.
NA, not applicable (this patient had only interictal spikes); M. male; F, female; 1, left; r, right; F, frontal; T, temporal; P, parietal; O, occipital. Letters in parenthesis indicate mild/partial involvement of the lobe.