Table 1.
Subject | Sex | Handedness | Age | Onset of total blindness | Cause of blindness | Residual vision | Psychophysics | fMRI |
---|---|---|---|---|---|---|---|---|
Eb1 | M | R | 38 years | 2 years* | Retinoblastoma | No | Yes | Yes |
Eb2 | F | R | 60 years | 0 years | Glaucoma | No | Yes | Yes |
Eb3 | F | R | 23 years | 0 years | Retinopathy of prematurity | Light perception | Yes | Yes |
Eb4 | M | R | 32 years | 3 years* | Glaucoma | No | Yes | Yes |
Eb5 | M | R | 37 years | 0 years | Retinopathy of prematurity | No | Yes | Yes |
Eb6 | M | R | 23 years | 0 years | Amaurosis | Light perception | Yes | Yes |
Eb7 | M | R | 30 years | 0 years | Retinopathy of prematurity | Light perception | Yes | Yes |
Eb8 | F | R | 23 years | 0 years | Retinopathy of prematurity | Light perception | Yes | Yes |
Eb9 | M | R | 36 years | 2 years* | Retinoblastoma | No | Yes | Yes |
Eb10 | F | R | 45 years | 0 years | Congenital unknown disease | Yes | Yes | Yes |
Eb11 | F | R | 62 years | 7 years* | Congenital cataract | No | Yes | Yes |
Eb12 | M | R | 28 years | 0 years | Microphthalmia | No | Yes | Yes |
Eb13 | M | L | 26 years | 0 years | Anophthalmia | No | Yes | No |
Eb14 | M | R | 54 years | 0 years | Glaucoma | No | Yes | No |
Eb15 | M | R | 44 years | 0 years | Retinopathy of prematurity | No | No | Yes |
Eb16 | M | R | 37 years | 0 years | Retinopathy of prematurity | No | No | Yes |
Eb17 | F | R | 58 years | 0 years | Congenital unknown disease | Light perception | No | Yes |
Eb18 | F | R | 50 years | 0 years | Chorioretinal atrophy | Light perception | No | Yes |
Eb19 | M | R | 29 years | 0 years | Retinopathy of prematurity | No | No | Yes |
The “Psychophysics” and “fMRI” columns indicate subject participation in the psychophysical and fMRI experiments, respectively.
Vision of these subjects was substantially reduced well before the clinical diagnosis of total blindness (see the main text).