Table 1.
Reported cases | Age/sex | Symptoms | Location | Treatment | Outcome |
---|---|---|---|---|---|
Yanagihara et al. [2] | 41/M | Recurrent FP | ME/facial nerve | Surg | NED |
Benton et al. [3] | 37/M | Ota | ME/M | Surg/Radio | NED at 1 yr |
Nam et al. [4] | 24/F | Ota/HL/Dizz/RP | M/dura | Surg/Radio | NED at 1 yr |
Wiseman et al. [5] | 4/M | FP | ME/M/facial nerve | Surg | NED |
39/M | HL | ME/M/Lab/IAC | Surg | NED | |
Mulder et al. [6] | 38/F | HL | ME/M/Lab/IAC | Surg | NED |
50/F | HL | ME/M/Lab/IAC | Surg | Relapsed | |
Janicki et al. [7] | 55/M | Oto/Tinn/vertigo | ME/M/dura/petrous apex | Radio | NED at 2 mo |
39/F | Ota/Oto/vertigo/HL | ME/M | Surg/steroid/IST | Relapsed at 4 mo | |
Schönermark [8] | 49/F | Ota/Oto/HL | ME/M/Lab | Surg/steroid | NED at 30 mo |
35/F | FP/HL/Ota/Oto | ME/M/Lab | Surg/IST | NED at 2 yrs | |
59/M | Ota/Oto/HL | ME/M/Lab | Surg/IST/steroid | Died of the disease | |
Gasparotti et al. [9] | 26/M | Vertigo | M/Teg/Sig/dura | Surg | NED |
Williamson et al. [10] | 49/M | HL/Oto | ME/M/Teg/MCF/Lab | Surg/steroid | NED at 6 mo |
Cho et al. [11] | 42/F | Hea/HL/FP/diplopia/ visual dimness |
M/ME/dura/tentorium/ cavernous sinus |
Steroid | Remission at 3 mo |
Cho et al. [12] | 55/F | HL/Oto | ME/M | Surg | NED at 1 yr |
Lee et al. [13] | 39/M | HL/RP/diplopia | M/petrous apex/lung | Surg/steroid | NED at 1 yr |
Lee et al. [14] | 28/F | FP/Ota | M | Surg | NED at 3 yrs |
Strasnick and Vaughan [15] | 65/F | HL/Dizz/Tinn | M/Sig/MCF | Surg/Radio/steroid | NED at 8 yrs |
40/M | HL/facial pain/ ear fullness |
Petrous apex/M/ME | Surg/Radio | NED at 10 yrs | |
Coulson et al. [16] | 60/M | HL/Oto/Ota/FP | M/ME/brain parenchyma | Steroid | NED at 18 mo |
Lee et al. [17] | 7/F | HL/ear-fullness | ME/M | Surg | NED at 6 mo |
Allona et al. [18] | 28/M | Hea | Petrous apex/Sig | No | Remission at 1 yr |
Ajibade et al. [19] | 41/M | Ota/HL/Tinn/Oto | M/Teg/dura | Surg/steroid | Relapsed at 4 mo |
Curry et al. [20] | 2.5/M | Ota/fluctuating FP | ME/M/Lab | Surg/steroid | NED at 1.5 yrs |
Santaolalla-Montoya et al. [21] | 75/M | Hea/Oto/HL | ME/M/Petrous apex/dura | Surg/steroid | Died of the disease |
Galindo et al. [22] | 28/M | HL/Hea/Ota | Petrous apex/ME | No | Remission at 3 yrs |
Goh et al. [23] | 27/F | Ota/HL | ME/M (bilateral) | Surg/steroid | NED at 3 yrs |
Vasileios et al. [24] | 19/M | auricular polyp | ME/External ear | Surg | NED at 6 mo |
Ota: otalgia; HL: hearing loss; Dizz: dizziness; Tinn: tinnitus; RP: retrobulbar pain; Oto: otorrhea; Hea: headache; FP: facial palsy; Exo: exophthalmos; ME: middle ear; M: mastoid; Lab: labyrinth; Teg: tegmen tympani; MCF: middle cranial fossa; Sig: sigmoid sinus; IAC: internal auditory canal; Surg: surgery; Radio: radiotherapy; IST: immunosuppressive therapy; NED: no evidence of disease at followup.