Table 1. Clinical features of EA-2 family.

Pt.no	Age	Age of onset	Trigger	Duration	Frequencies	Abdominalpain	Gait ataxia	Additional symptoms	interictal symptoms
2	74	5	−	several; ds	3–4/y	+	+	slurred speech, nystagmus, myokymia,nausea and vomiting	−
3	54	35	emotion, sports	6 hs	1–2/m	−	+	dysarthria, nystagmus, blurred vision, visualfield defects, seizure, myokymia, dystonia, weakness,migraine, dizziness, nausea, vomiting,sweating
4	47	12	−	mins	1/1–4 w	+	+	dysarthria, vertigo, nausea and vomiting	+
5	44	6–7	−	up to 5 mins	1/ys	+	−	nausea and vomiting	+
6	39	7	−	till sleep	½–3 m	−	−	diplopia, headache, vertigo, lower extremitynumbness	+
7	21	15	−	1 h	1/2–3 d	+	+	dysarthria,diplopia,dizziness, nauseaand vomiting
8	25	4	emotion, frightened sports	3–4 hs	1/1–2d	−	+	dysarthria,diplopia,defects of visualfield, myotonia,myokymia sometime,vertigo,weakness, dizziness, obvious rightarm tremor	+
9	21	17	tired	mins	1/1–2 w	−	−	diplopia, migraine, tinnitus sometime	+
10	21	7	frightened, sports	till sleep	irregular		+	dysarthria, diplopia,headaches, vertigo,myokymia, tinnituspalpitation, sweat, unable to hold items	−
11	16	5	−	hs	1/y	+	+	dysarthria, weakness, migraine, nauseaand vomiting
12	16	13	sports	mins	1/m	−	−	dysarthria,diplopia, vertigo, tinnitus (low noise)	−

Pt no = patients number; min = minute; h = hour; d = days; w = week; m = month; y = year.