Table 1. Six haemophilic pseudotumours of the maxillary bone reported in the literature.
Author | Sex (M/F)/age (years) | History | Symptoms | Haemophilia | Laterality | Imaging findings | Treatment | Follow-up |
de Sousa et al (1995) [1] | M/1 | Tibia HP, nasal trauma 6 years previously | None (incidental finding) | A (<1% Factor VIII) | Left | Radiolucent lesion (CT) | Curettage | Healing (2 years) |
Zheng K (1997) [2] | M/26 | Tibia HP | None (incidental finding) | A (11% Factor VIII) | Left | Radiolucent lesion (radiograph) | Curettage | Not specified |
Stevenson and Keast (2002) [8] | M/75 | COAD, chronic atrial fibrillation, aortic valve replacement surgery | Spontaneous epistaxis | No haemophilia | Right | Soft-tissue mass associated bone expansion and destruction (CT) | Curettage, radiotherapy | No recurrence (18 months) |
Steele et al (2004) [7] | M/0.5 | None | Cheek swelling, eye tearing for 3 weeks | A (<1% Factor VIII) | Left | Hypodense mass with peripheral nodular enhancement (CT), hypointense lesion with hyperintense rim on T1 weighted image (MRI) | Curettage, Factor VIII therapy | Not specified |
Lima et al (2008) [9] | M/12 | Bone cyst of the radius | Spontaneous gingival bleeding for 2 months | A (14% Factor VIII) | Left | Osteolytic lesion with bony cortical preservation, (panoramic radiography and CT) | Curettage, Factor VIII therapy | No recurrence (9 months) |
Xue et al (2011) [10] | M/24 | None | Pain, dysfunction for 1 month | A (<5% Factor VIII) | Right | Soft-tissue lump with erosion bony cortex | Replacement therapy | Resolution |
COAD, chronic obstructive airway disease; F, female; HP, haemophilic pseudotumours; M, male.