Table 2.

Baseline characteristics on electrocardiography in 24 MPS patients. MPS I (H/S) = MPS I Hurler and MPS I Scheie patients. Bpm = beats per minute

	Baseline overall	MPS I (H/S)	MPS II	MPS VI
ECG data
Rhythm
Sinus	24 (100%)	8 (100%)	6 (100%)	10 (100%)
Sinus tachycardia	1 (4%)	1 (13%)	0 (0%)	0 (0%)
Heart rate (bpm)	107 [78-155]	120 [100-155]	118 [80-150]	93 [78-125]
PR interval (ms)	140 [110,180]	130 [120,150]	145 [110,180]	140 [120,180]
Prolonged PR	3 (13%)	0 (0%)	2 (33%)	1 (10%)
QRS duration (ms)	80 [70,100]	80 [70,80]	80 [80-00]	80 [70,100]
Prolonged QRS	3 (13%)	0 (0%)	2 (%)	1 (10%)
QTc interval (ms)	415 [378,453]	402 [390, 417]	440 [412,453]	422 [378, 441]
Prolonged QTc	0 (0%)	0 (0%)	0 (0%)	0 (0%)
Incomplete bundle branch block	2 (8%)	0 (0%)	1 (17 %)	1 (10%)
Left fascicular block	2	1 (13%)	0 (0%)	1 (10%)
Left atrial enlargement	2 (8%)	0 (0%)	1 (17 %)	1 (10%)
Right-ventricular hypertrophy	1 (4%)	1 (13 %)	0 (0%)	0 (0%)
Left-ventricular hypertrophy	1 (4%)	0 (0%)	0 (0%)	1 (10%)
Repolarisation disorder	2 (8%)	0 (0%)	1 (17%)	1 (10%)