Survival and body weight was improved post transplant in intermediate maple syrup urine disease (iMSUD) mice. Vertical gridlines at 35 and 100 days indicates sacrifice points. (A) Survival of iMSUD mice given human amnion epithelial cell transplant (hAEC Tx) and untreated controls (WT and iMSUD). (B) Weekly body weight (g) beginning at weaning (21 days). (C) Human DNA quantified in mouse liver. WT, wildtype; ND, none detected; ***, p<0.001, one-way ANOVA, Tukey post-hoc compared to iMSUD. **p<0.01, unpaired t-test.