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. Author manuscript; available in PMC: 2014 Feb 1.
Published in final edited form as: Circ Arrhythm Electrophysiol. 2012 Sep 28;6(1):228–237. doi: 10.1161/CIRCEP.111.962050

Figure 2.

Figure 2

Non-Coronary Pattern of Delayed Gadolinium Enhancement imaged with Cardiac MRI in Familial DCM. Short axis Cardiac MRI (CMR) images reveal circumferential subepicardial delayed enhancement (DE) of gadolinium (arrows) in a young patient with familial DCM and palmoplantar keratoderma caused by a DSP mutation. The pattern of delayed enhancement of gadolinium is not specific for genetic heart disease, but is distinct from ischemic cardiomyopathy.

LV = left ventricle; RV = right ventricle.

Images courtesy of Ravi Shah, MD and Raymond Kwong, MD, Brigham and Women’s Hospital, Boston, MA.